SACROCOCCYGEAL CHORDOMA

A sacrococcygeal chordoma is a rare malignant tumor that originates from remains of the notochord, a vestigial transitory organ that builds the first model of the spine during embryonic development. Because of the existence of notochordal remains in the clivus and sacrococcygeal areas, they mostly develop in the sacrococcygeal and spheno-occipital regions.

Chordomas grow slowly, but they can relapse and have an aggressive clinical course, metastasizing to other organs, such as the lungs, lymph nodes, liver, bones, skin, and skeletal muscle, or tissues adjacent to the primary tumor via direct extension or local recurrence after surgical excision.

SYMPTOMS

The location of the chordoma determines the symptoms. Among the signs and symptoms are:

  • Nerve or muscle weakness in the back, arm, or leg
  • Problems with vision, like double vision
  • Headaches
  • Pain
  • Nosebleeds

Sacrococcygeal chordoma often does not cause symptoms until the tumor is huge, and a lump is sometimes the first indication of chordoma.

DIAGNOSIS

Sacrococcygeal chordoma symptoms may differ considerably depending on where the chordoma starts in your spine. You may suffer headaches or double vision if the chordoma spreads to the base of the skull. Chordoma around the tailbone may cause leg discomfort and difficulty managing your bladder or intestines. The following tests and techniques are used to diagnose chordoma:

  • Imaging. If you have chordoma symptoms, your doctor will use an MRI to create a picture of your spine to determine the size and location of the tumor. A CT scan can also be used to evaluate whether or not the cancer has developed.
  • Biopsy. To determine if the tumor is chordoma, your physician will do a biopsy, which involves extracting a tiny sample from the tumor using a needle. A pathologist will use a microscope to study cells from the sample to identify what type of tumor it really is. Chordoma cells resemble notochord cells when seen under a microscope.

TREATMENT

Sacrococcygeal chordoma therapy is determined by the cancer’s size and location, as well as whether it has infiltrated nerves or other tissues. Surgery, radiation treatment, radiosurgery, and targeted therapies may all be options.

If the chordoma affects the lower part of the spine (sacrum), the following treatments may be considered:

  • Surgery.
  • Radiation treatment.
  • Radiosurgery.
  • Targeted therapy

If the chordoma affects the region where the spine meets the skull (skull base), the following treatments may be considered:

  • Surgery.
  • Radiation treatment.
  • New therapies.

Related Articles

TETRALOGY OF FALLOT

Overview and FactsTypes and SymptomsDiagnosis & MedicationsOverview and Facts Tetralogy of Fallot is a congenital heart defect that affects the [...]

TRICHINOSIS

Overview and FactsTypes and SymptomsDiagnosis & MedicationsOverview and Facts Trichinosis, also known as trichinellosis, is a parasitic infection caused by [...]

TRIGEMINAL NEURALGIA

Overview and FactsTypes and SymptomsDiagnosis & MedicationsOverview and Facts Trigeminal neuralgia is a neurological condition characterized by severe facial pain. [...]