Infantile perianal pyramidal extrusion (IPPE), also known as infantile anal protrusion, is a rare condition characterized by the protrusion of anal mucosa through the anus in infants and young children. While the exact cause of IPPE is not well understood, it is believed to involve a combination of anatomical factors, bowel habits, and increased intra-abdominal pressure. Understanding the causes, symptoms, diagnosis, treatment, and management of infantile perianal pyramidal extrusion is essential for appropriate clinical management and alleviation of symptoms.