LYSOSOMAL STORAGE DISORDERS

TYPES

Other common types of leg ulcer include:

• Gaucher disease
• Fabry disease
• Niemann-Pick disease
• Hunter syndrome
• Glycogen storage disease II (Pompe disease)
• Tay-Sachs disease

SYMPTOMS

Even though the signs and symptoms change from one disorder to the next in this gathering, symptoms happen for each situation due to an enzyme deficiency that represses the capacity of the lysosomes present in every one of the body’s cells to play out their ordinary function. The lysosomes work as the essential stomach-like related units inside cells. They can degrade complex parts into less complex ones.  For proteins (substrates) to be degraded into less complex segments, lysosomes must carry out their functions inside each cell. At the point when this procedure doesn’t happen, the substrate starts to aggregate in the cells. That is the reason these disorders are designated “storage diseases”. The side effects of lysosomal storage disorders are commonly progressive over some time.

DIAGNOSIS

Latex allergy is diagnosed by an allergy blood test.

TREATMENT

The best treatment for latex sensitivity is avoiding it as much as possible. If you have serious latex sensitivity response you should:

• Wear medicinal identification tags to signify that you have a  latex allergy.
• Havean epinephrine (adrenaline) auto-injector on-hand for emergency treatment.

Healthcare workers with a past latex sensitivity who must wear gloves should quit wearing latex gloves. Their colleagues ought to likewise not utilize latex gloves, but instead change to manufactured, synthetic non-latex gloves.

Patients with latex hypersensitivity are in danger of asthma on exposure to latex-containing pressurized canned sprays. They should attempt to maintain a strategic distance from zones where powdered latex gloves or other latex items are utilized.

The most ideal approach to treat this kind of hypersensitivity is to avoid latex. In case you’re exposed, escape from it ASAP.