There are two main types of Double-Inlet Left Ventricle (DILV), known as DILV with transposition of the great arteries (TGA) and DILV with normally related great arteries. Here’s an overview of each type:
1. DILV with Transposition of the Great Arteries (TGA)
In this type, the blood vessels that carry blood away from the heart, namely the aorta and pulmonary artery, are switched. The aorta is connected to the right ventricle, which pumps deoxygenated blood to the body, while the pulmonary artery is connected to the left ventricle, which pumps oxygenated blood to the lungs. This leads to a mixed circulation of oxygenated and deoxygenated blood.
2. DILV with Normally Related Great Arteries
In this type, the aorta and the pulmonary artery are in their usual positions, with the aorta connected to the left ventricle and the pulmonary artery connected to the right ventricle. However, both the right and left atria still connect to the left ventricle. The left ventricle then receives blood from both atria, resulting in a mixture of oxygenated and deoxygenated blood being pumped to the body.
It’s important to note that DILV can also be associated with other heart defects, such as ventricular septal defects (VSDs) or atrial septal defects (ASDs), which further complicate the circulation of blood within the heart.
The specific type of DILV, along with associated abnormalities, anatomical variations, and the overall condition of the individual, will influence the treatment approach and long-term management. Consulting with a pediatric cardiologist is crucial to obtain an accurate diagnosis, determine the appropriate treatment plan, and provide ongoing care for individuals with DILV.
The symptoms of Double-Inlet Left Ventricle (DILV) can vary depending on the severity of the defect and associated abnormalities. Here are some common symptoms that may be observed in individuals with DILV:
- Cyanosis: Infants with DILV may have a bluish tint to their skin, lips, or nails due to insufficient oxygenation of the blood.
- Rapid breathing: Infants may exhibit rapid and labored breathing, which can be a sign of the heart’s inability to pump oxygenated blood effectively.
- Poor feeding: Infants may have difficulty with feeding, such as tiring easily during feeds or having trouble gaining weight.
- Failure to thrive: Infants may not grow at the expected rate and may have difficulty reaching developmental milestones.
- Fatigue and exercise intolerance: As children with DILV grow older, they may experience fatigue and have difficulty keeping up with physical activities due to inadequate oxygen supply to the body.
- Recurrent respiratory infections: Individuals with DILV may be more prone to respiratory infections, such as pneumonia or bronchitis, due to compromised lung function.
It’s important to note that these symptoms can also be present in other heart conditions, and a proper diagnosis by a healthcare professional, such as a pediatric cardiologist, is necessary to determine the underlying cause and develop an appropriate treatment plan.
If you or someone you know is experiencing any symptoms or concerns related to DILV, it is advisable to seek medical attention promptly for a thorough evaluation and guidance.