Primary pulmonary hypertension is hypertension in the lungs. It’s an uncommon lung problem that arises when there is increased pressure in the blood vessels of the lungs due to their narrowing and increased load. The pulmonary arteries are the ones that carry blood from the other parts of the body to the heart and lungs so that there will be oxygen and carbon dioxide exchange. If there is primary pulmonary hypertension, circulation is poor and there is difficulty of breathing.

Pneumonic hypertension can lead to heart failure if untreated.

There are 5 types of pulmonary arterial hypertension.

Group 1 Pulmonary Arterial Hypertension

Pulmonary hypertension is the main type of the illness that isn’t alluded to pulmonary hypertension.

It can be classified as idiopathic, inherited, or can be due to abuse of opiates or poisons or as the effect of another disease like scleroderma, lupus, or HIV.

Group 2 Pulmonary Hypertension

This group involves patients who have developed pulmonary hypertension because of left heart disorders, for example, left ventricular diastolic dysfunction or valvular disease.

Group 3 Pulmonary Hypertension

This group involves to patients who have pulmonary hypertension due to hypoxia or another lung problem like for COPD, interstitial lung diseases, and high-altitude exposure.

Group 4 Chronic Thromboembolic Pulmonary Hypertension

This can result from blood clumps that form in the lungs.

Group 5 Pulmonary Hypertension due to other disorders

This group is made up of Individuals with other problems and conditions, such as blood disorders, metabolic problems, thyroid disease or kidney illness.



The following are the most widely recognized side effects for primary pulmonary hypertension. Symptoms can grow so gradually that you can have it for a considerable length of time without knowing it. Nonetheless, every individual may encounter manifestations in an unexpected way. Symptoms may include:

  • Bluish discoloration of the lips and skin
  • Chest pain
  • Dizziness
  • Dry cough
  • Extreme tiredness
  • Fainting
  • Fluttering fast beating heart
  • Swelling in the lower legs
  • Trouble breathing or shortness of breath


Primary pulmonary hypertension is occasionally found in a routine medical exam. It can further lead to other conditions that affect the heart and lungs.

It might be diagnosed when different diseases are excluded. Tests may include:

  • Chest X-ray
  • ECG
  • Echocardiogram
  • Pulmonary function tests
  • Perfusion lung scan
  • Right heart catheterization
  • Blood tests for oxygen levels in the blood, liver and kidney function




There is no remedy for primary pulmonary hypertension. Treatment endeavors to oversee symptoms and may include at least one of the following:

  • Medicines such as anticoagulants or blood thinners
  • Diuretics to reduce swelling
  • Calcium channel blocking medicines or vasodilator drugs
  • Pulmonary artery specific therapy, such as ambrisentan, sildenafil, and epoprostenol
  • Oxygen therapy
  • Lung transplant




























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